Behçet disease – although rare can be present in children
نویسنده
چکیده
Introduction The child’s history reveals frequent faringitis accompanied by oral lesions (4-5 episodes/year), billatreal ankle joint swelling and weight loss. Behçet disease (BD) is characterized by a triple-symptom complex of recurrent oral aphthous ulcers, genital ulcers, and uveitis. Hippocrates may have described Behçet disease in the fifth century BC; however, the first description of the syndrome was attributed to the Turkish dermatologist Hulusi Behçet in 1924. In 1930, the Greek physician Adamantiades reported a patient with inflammatory arthritis, oral and genital ulcers, phlebitis, and iritis. Since then, the syndrome has been referred to as Behçet disease.
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